Noncompaction cardiomyopathy and heterotaxy syndrome

HR Martinez, SM Ware, MS Schamberger… - Progress in pediatric …, 2017 - Elsevier
Left ventricular noncompaction cardiomyopathy (LVNC) is characterized by compact and
trabecular layers of the left ventricular myocardium. This cardiomyopathy may occur with
congenital heart disease (CHD). Single cases document co-occurrence of LVNC and
heterotaxy, but no data exist regarding the prevalence of this association. This study sought
to determine whether a non-random association of LVNC and heterotaxy exists by
evaluating the prevalence of LVNC in patients with heterotaxy. In a retrospective review of …